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A Rare Cause of Acute Abdominal Pain Herlyn-Werner-Wunderlich Syndrome   
Yazarlar
Ramazan Aydin
Öğr. Gör. Ayşe ÖZDEMİR
Kastamonu Üniversitesi
Bahadir Ozturk
Meltem Ceyhan Bilgici
Migraci Tosun
Özet
Herlyn-Werner-Wunderlich (HWW) syndrome is a rare müllerian duct anomaly with uterus didelphys, unilateral obstructed hemivagina, and ipsilateral renal agenesis. Patients with this syndrome generally present after menarche with pelvic pain and mass and, rarely, primary infertility in later years. Strong suspicion and knowledge of this syndrome are mandatory for an accurate diagnosis. A 14-year-old female patient presented with acute retention of urine and abdominopelvic pain. Her condition was diagnosed with the use ultrasonography and magnetic resonance imaging as a case of HWW syndrome. She was treated with vaginal hemiseptal resection. The HWW syndrome should be considered among the differential diagnoses in girls with renal anomalies presenting with pelvic mass, symptoms of acute abdominal pain, and acute urinary retention.
Anahtar Kelimeler
mullerian duct anomaly,acute urinary retention,acute abdominal pain,Herlyn-Werner-Wunderlich syndrome
Makale Türü Özgün Makale
Makale Alt Türü ESCI dergilerinde yayımlanan tam makale
Dergi Adı PEDIATRIC EMERGENCY CARE
Dergi ISSN 0749-5161
Makale Dili İngilizce
Basım Tarihi 10-2014
Cilt No 30
Sayı 1
Sayfalar 40 / 42
Doi Numarası 10.1097/PEC.0000000000000052
BM Sürdürülebilir Kalkınma Amaçları
Atıf Sayıları
WoS 7
A Rare Cause of Acute Abdominal Pain Herlyn-Werner-Wunderlich Syndrome

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